Dandy-Walker malformation is characterised by agenesis or hypoplasia of the cerebellar vermis, cystic dilatation of the fourth ventricle, and enlargement of the posterior fossa. Approximately 70- 90% of patients have hydrocephalus. Lissencephaly is characterised by absence (agyria) or incomplete development (pachygyria) of the gyri of the cerebral cortex, causing the brain__ampersandsign#39;s surface to appear unusually smooth. Our case demonstrates Dandy Walker malformation with partial corpus callosal agenesis, hydrocephalus and Lissencephaly.